Late Onset Spinocerebellar Ataxia

What are the signs & symptoms that develop in affected dogs?

Signs of cerebellar disease include: dogs have an uncoordinated gait (ataxia) with stilted "toy soldier" leg movements. They can display "intention tremors," where a stretched out limb or head shakes more and more violently as it approaches its target. At rest, dogs sometimes display a "truncal sway;" their spinal muscles have lost their fine-tuning, pulling the spine (and everything attached to it) back and forth in a struggle to maintain balance. The muscles of the eyes have also lost this fine-tuning, leading to a rhythmic eye flicking (nystagmus).

When do signs and symptoms develop?

Unlike other SCAs in the Russell Terriers, loSCA begins between six and twelve months of age.

How do vets diagnose this condition?

Unless a genetic basis is suspected due to the age, breed, or history of the dog, diagnostics must be performed to rule out infectious, inflammatory, or neoplastic causes.

How is this condition treated?

During the first few months of the disease, symptoms can become progressively more severe. Though the disease can stabilize to some degree with time, episodes of worsening have been reported. As walking becomes extremely difficult towards the end stages of the disease, euthanasia is usually elected.

What actions should I take if my dog is affected?

• Keeping your affected dog comfortable and giving them the best quality of life you can are the only actions you can take at home.